Xanthogranulomatous Pyelonephritis (XGPN) Presenting as Renal Lump in Infant: Rare Presentation

Rahul Ghule, Ram Daga, Jaydeep

Abstract

Background: Xanthogranulomatous pyelonephritis (XGPN) is an unusual suppurative granulomatous reaction to chronic renal infection. It usually presents with symptoms of infections. It is rare entity especially in childhood. Case: We are reporting case of xanthogranulomatous pyelonephritis in 2 month male baby presented as left renal mass without signs of infections. On imaging it shows multicystic, heterogeneous, non-enhancing left renal mass. Conclusion: XGPN, itself is a rare entity presenting in infant/childhood of which presentation solely as renal lump without any signs and symptoms of urosepsis, UTI. Hence even in neonate/childhood one should consider it as one of D/D presenting as renal mass.

Relevant Publications in Journal of Rare Disorders: Diagnosis & Therapy